Human LYAG/GAA ELISA Kit (Colorimetric)

ELISA: Human LYAG/GAA ELISA Kit (Colorimetric) [NBP2-82448] - Samples were spiked with high concentrations of Human LYAG/GAA and diluted with Reference Standard & Sample Diluent to produce samples with values within the range of the assay.

ELISA: Human LYAG/GAA ELISA Kit (Colorimetric) [NBP2-82448] - Standard Curve Reference

• Reactivity: Hu
• Applications: ELISA
• Suitable Sample Type: Serum, plasma, cell supernatant, and other biological fluids
• Standard Curve Range: 0.16 - 10 ng/mL
• Sensitivity: 0.09 ng/mL

Human LYAG/GAA ELISA Kit (Colorimetric) Summary

• Specificity: This kit recognizes Human LYAG/GAA in samples. No Significant cross-reactivity or interference between Human LYAG/GAA and analogues was observed.
• Standard Curve Range: 0.16 - 10 ng/mL
• Sensitivity: 0.09 ng/mL
• Assay Type: Sandwich-ELISA
• Inter-Assay: CV% < 5.29
• Intra-Assay: CV% < 5.01
• Spike Recovery: 90-107%
• Sample Volume: 100 ul
• Kit Type: ELISA Kit (Colorimetric)
• Gene: GAA

Applications/Dilutions

• Dilutions:
  • ELISA

Packaging, Storage & Formulations

• Storage: Storage of components varies. See protocol for specific instructions.

Alternate Names for Human LYAG/GAA ELISA Kit (Colorimetric)

• Acid alpha-Glucosidase
• Acid Maltase
• Aglucosidase alfa
• EC 3.2.1.20
• GAA
• glucosidase, alpha; acid
• LYAG
• Lysosomal alphaGlucosidase
• Lysosomal alpha-Glucosidase

Background

GAA encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq]

Limitations

This product is for research use only and is not approved for use in humans or in clinical diagnosis. ELISA Kits are guaranteed for 6 months from date of receipt.

Bioinformatics

• Gene Symbol: GAA