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HAF008). Specific bands were detected for Lysosomal a-Glucosidase at approximately 72 kDa, 75 kDa, and 105 kDa (as indicated). This experiment was conducted under reducing conditions and using Immunoblot Buffer Group 1." class="big_lightbox" target="_blank">
VC003). Before incubation with the primary antibody, tissue was subjected to heat-induced epitope retrieval using Antigen Retrieval Reagent-Basic (Catalog # CTS013). Tissue was stained using DAB (brown) and counterstained with hematoxylin (blue). Specific staining was localized to cytoplasm in convoluted tubules. View our protocol for IHC Staining with VisUCyte HRP Polymer Detection Reagents." class="big_lightbox" target="_blank">
GAA encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq]
![Western Blot LYAG/GAA Antibody (2489C) [Unconjugated]](http://images.novusbio.com/images/antibody/Lysosomal_alphaGlucosidase_MAB8329_Western_Blot_23905.jpg)
![Enzyme Activity LYAG/GAA [Unconjugated]](http://images.novusbio.com/fullsize/8329-gh_recombinant-human-lysosomal-alpha-glucosidase-gaa-cf-enzyme-activity-622023983.jpg)
![Enzyme Activity LYAG/GAA [Unconjugated]](http://images.novusbio.com/fullsize/11400-gh_recombinant-mouse-lysosomal-alpha-glucosidase-gaa-cf-enzyme-activity-7920239280..jpg)
![Immunohistochemistry LYAG/GAA Antibody (2489C) [Unconjugated]](http://images.novusbio.com/images/antibody/Lysosomal_alphaGlucosidase_MAB8329_Immunohistochemistry_23608.jpg)
![Enzyme Activity LYAG/GAA [Unconjugated]](http://images.novusbio.com/fullsize/8329-gh_recombinant-human-lysosomal-alpha-glucosidase-gaa-cf-enzyme-activity-6220239264.jpg)
![SDS-Page LYAG/GAA [Unconjugated]](http://images.novusbio.com/fullsize/8329-gh_recombinant-human-lysosomal-alpha-glucosidase-gaa-cf-sds-page-62202393418.jpg)
![SDS-Page LYAG/GAA [Unconjugated]](http://images.novusbio.com/fullsize/11400-gh_recombinant-mouse-lysosomal-alpha-glucosidase-gaa-cf-sds-page-79202393758.jpg)
