HADHA Products

Antibodies
HADHA Antibody
HADHA Antibody
NBP1-33588
Species: Hu, Mu, Rt
Applications: WB, ICC/IF, IHC, IHC-P
Host: Rabbit Polyclonal
HADHA Antibody
HADHA Antibody
NBP1-83387
Species: Hu, Mu
Applications: WB, ICC/IF, IHC, IHC-P
Host: Rabbit Polyclonal
HADHA Antibody
HADHA Antibody
NBP2-30077
Species: Hu
Applications: WB, Flow, IHC-P
Host: Rabbit Polyclonal
Lysates
HADHA Overexpression Lysate ( ...
HADHA Overexpression Lysate (Denat...
H00003030-T01
Species: Hu
Applications: WB
HADHA Overexpression Lysate ( ...
HADHA Overexpression Lysate (Native)
NBP2-04152
Applications: WB
Proteins
HADHA Recombinant Protein
HADHA Recombinant Protein
H00003030-P01
Species: Hu
Applications: WB, ELISA, PA
HADHA Recombinant Protein Ant ...
HADHA Recombinant Protein Antigen
NBP1-83387PEP
Species: Hu
Applications: AC

Description

HADHA encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Bioinformatics

Entrez Human
Uniprot Human
Human
Human
Product By Gene ID 3030
Alternate Names
  • TP-alpha
  • ECHA
  • trifunctional enzyme subunit alpha, mitochondrial
  • 3-oxoacyl-CoA thiolase
  • mitochondrial trifunctional protein, alpha subunit
  • 3-ketoacyl-Coenzyme A (CoA) thiolase, alpha subunit
  • mitochondrial trifunctional enzyme, alpha subunit
  • HADH
  • mitochondrial long-chain L-3-hydroxyacyl-Coenzyme A (CoA) dehydrogenase, alphasubunit
  • 78 kDa gastrin-binding protein
  • mitochondrial long-chain 2-enoyl-Coenzyme A (CoA) hydratase, alpha subunit
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme Athiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit
  • long-chain-3-hydroxyacyl-CoA dehydrogenase
  • LCHAD
  • long-chain 2-enoyl-CoA hydratase
  • LCEH
  • gastrin-binding protein
  • GBP
  • MTPATP-ALPHA
  • MGC1728
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase(trifunctional protein), alpha subunit

Pathways for HADHA

View related products by pathway and learn more about each of the pathways below.

Fatty Acid Oxidation
Fatty Acid Beta-oxidation
Localization
Senescence
Translation
Hypersensitivity
Pathogenesis
Muscle Atrophy

PTMs for HADHA

Learn more about PTMs related to HADHA.

Oxidation
Phosphorylation
Reduction

Bioinformatics Tool for HADHA

Discover related pathways, diseases and genes to HADHA. Need help? Read the Bioinformatics Tool Guide for instructions on using this tool.
 
Vizit™, under license from BioVista Inc.