GCSH Products

Antibodies
GCSH Antibody
GCSH Antibody
NBP1-85842
Species: Hu, Mu, Rt
Applications: WB, IHC, IHC-P
Host: Rabbit Polyclonal
GCSH Antibody (M2)
GCSH Antibody (M2)
H00002653-M02
Species: Hu
Applications: WB, ELISA
Host: Mouse Monoclonal
GCSH Antibody (3D8-A12)
GCSH Antibody (3D8-A12)
H00002653-M01
Species: Hu
Applications: WB, ELISA
Host: Mouse Monoclonal
Lysates
GCSH Overexpression Lysate (N ...
GCSH Overexpression Lysate (Native)
NBL1-11020
Applications: WB
Proteins
GCSH Recombinant Protein Anti ...
GCSH Recombinant Protein Antigen
NBP1-85842PEP
Species: Hu
Applications: AC
Recombinant Human GCSH Protei ...
Recombinant Human GCSH Protein
NBP1-72520
Species: Hu
Applications: PAGE
RNAi
GCSH RNAi
GCSH RNAi
H00002653-R01
Species: Hu
Applications: RNAi, RNAi SP

Description

The enzyme system for cleavage of glycine (glycine cleavage system; EC 2.1.2.10), which is confined to themitochondria, is composed of 4 protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase;MIM 238300), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme; MIM238310), and L protein (a lipoamide dehydrogenase; MIM 238331). Glycine encephalopathy (GCE; MIM 605899), also callednonketotic hyperglycinemia (NKH), may be due to a defect in any one of these enzymes.(supplied by OMIM)

Bioinformatics

Entrez Human
Uniprot Human
Human
Human
Human
Product By Gene ID 2653
Alternate Names
  • mitochondrial glycine cleavage system H-protein
  • lipoic acid-containing protein
  • glycine cleavage system H protein, mitochondrial
  • GCE
  • NKH
  • glycine cleavage system protein H (aminomethyl carrier)

PTMs for GCSH

Learn more about PTMs related to GCSH.

Cleavage

Bioinformatics Tool for GCSH

Discover related pathways, diseases and genes to GCSH. Need help? Read the Bioinformatics Tool Guide for instructions on using this tool.
 
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