Species: Hu, Mu, Rt
Applications: WB, ICC/IF, IHC
Host: Mouse monoclonal
Species: Hu, Mu, Rt
Applications: WB, IHC
Host: Rabbit Polyclonal
Species: Hu, Mu
Applications: WB, ICC/IF, IHC
Host: Rabbit Polyclonal
Species: Hu
Applications: WB
Species: Hu
Applications: WB, ELISA, MA, AP
Species: Hu
Applications: WB, ELISA, MA, AP
Species: Hu
Applications: AC
Description
BBOX1 encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation.
Bioinformatics
| Entrez |
Human
|
| Uniprot |
Human
Human
Human
|
| Product By Gene ID |
8424 |
| Alternate Names |
- 2-oxoglutarate dioxygenase 1
- 2-oxoglutarate dioxygenase
- BBHgamma-butyrobetaine
- BBOXEC 1.14.11.1
- butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetainehydroxylase) 1
- gamma-BBH
- Gamma-BBH
- gamma-butyrobetaine dioxygenase
- Gamma-butyrobetaine hydroxylase
- Gamma-butyrobetaine
- G-BBH
|
