BBOX1 Products

Antibodies
Lysates
BBOX1 Overexpression Lysate
BBOX1 Overexpression Lysate
NBL1-07926
Species: Hu
Applications: WB
Proteins
Recombinant Human BBOX1 Prote ...
Recombinant Human BBOX1 Protein
H00008424-Q01
Species: Hu
Applications: WB, ELISA, PA, AP
Recombinant Human BBOX1 Prote ...
Recombinant Human BBOX1 Protein
H00008424-P01
Species: Hu
Applications: WB, ELISA, PA, AP
BBOX1 Recombinant Protein Ant ...
BBOX1 Recombinant Protein Antigen
NBP1-88695PEP
Species: Hu
Applications: AC

Description

BBOX1 encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation.

Bioinformatics

Entrez Human
Uniprot Human
Human
Human
Product By Gene ID 8424
Alternate Names
  • Gamma-butyrobetaine hydroxylase
  • 2-oxoglutarate dioxygenase
  • Gamma-butyrobetaine
  • gamma-BBH
  • Gamma-BBH
  • G-BBH
  • BBOXEC 1.14.11.1
  • 2-oxoglutarate dioxygenase 1
  • BBHgamma-butyrobetaine
  • gamma-butyrobetaine dioxygenase
  • butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetainehydroxylase) 1

Diseases related to BBOX1

Discover more about diseases related to BBOX1.

Malignant Neoplasms
Asthma
Lung Diseases

Pathways for BBOX1

View related products by pathway and learn more about each of the pathways below.

Transport
Translation
Lactation
Fatty Acid Oxidation

Bioinformatics Tool for BBOX1

Discover related pathways, diseases and genes to BBOX1. Need help? Read the Bioinformatics Tool Guide for instructions on using this tool.
 
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