Phenylalanine Hydroxylase Products

Antibodies
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody
NBP2-48615
Species: Hu, Mu, Rt
Applications: WB, IHC
Host: Rabbit Polyclonal
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody
NBP1-80917
Species: Hu
Applications: WB, IHC
Host: Rabbit Polyclonal
Phenylalanine Hydroxylase Ant ...
Phenylalanine Hydroxylase Antibody
NBP1-52084
Species: Hu, Mu, Rt, Bv, Ca
Applications: WB, ELISA
Host: Goat Polyclonal
ELISA Kits
Human Phenylalanine Hydroxyla ...
Human Phenylalanine Hydroxylase EL...
NBP2-81206
Species: Hu
Applications: ELISA
Lysates
Phenylalanine Hydroxylase 293 ...
Phenylalanine Hydroxylase 293T Cel...
H00005053-T01
Species: Hu
Applications: WB
Proteins
Recombinant Human Phenylalani ...
Recombinant Human Phenylalanine Hy...
H00005053-P01
Species: Hu
Applications: WB, ELISA, MA, PAGE, AP
Phenylalanine Hydroxylase Rec ...
Phenylalanine Hydroxylase Recombin...
NBP1-80917PEP
Species: Hu
Applications: AC
Phenylalanine Hydroxylase Rec ...
Phenylalanine Hydroxylase Recombin...
NBP2-48615PEP
Species: Hu
Applications: AC

Description

PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.

Bioinformatics

Uniprot Human
Human
Human
Alternate Names
  • EC 1.14.16
  • EC 1.14.16.1
  • PH
  • phe-4-monooxygenase
  • Phe-4-monooxygenase
  • phenylalanine 4-monooxygenase
  • phenylalanine hydroxylase
  • phenylalanine-4-hydroxylase
  • PKU
  • PKU1