PCCA Products

Antibodies
PCCA Antibody
PCCA Antibody
NBP2-13736
Species: Hu, Mouse
Applications: WB, IHC, IHC-P
Host: Rabbit Polyclonal
PCCA Antibody
PCCA Antibody
H00005095-B01P
Species: Hu
Applications: WB, ELISA
Host: Mouse Polyclonal
PCCA Antibody
PCCA Antibody
NBP2-19717
Species: Hu
Applications: WB, IHC, IHC-P
Host: Rabbit Polyclonal
Lysates
PCCA Overexpression Lysate (D ...
PCCA Overexpression Lysate (Denatu...
H00005095-T01
Species: Hu
Applications: WB
PCCA Overexpression Lysate (N ...
PCCA Overexpression Lysate (Native)
NBL1-14146
Applications: WB
Proteins
PCCA Recombinant Protein
PCCA Recombinant Protein
H00005095-P01
Species: Hu
Applications: WB, ELISA, PA
PCCA Recombinant Protein Anti ...
PCCA Recombinant Protein Antigen
NBP2-13736PEP
Species: Hu
Applications: AC
PCCA Recombinant Protein Anti ...
PCCA Recombinant Protein Antigen
NBP2-13735PEP
Species: Hu
Applications: AC

Description

PCCA is encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq]

Bioinformatics

Uniprot Human
Human
Human
Human
Product By Gene ID 5095
Alternate Names
  • EC 6.4.1
  • PCCase alpha subunit
  • Propanoyl-CoA:carbon dioxide ligase subunit alpha
  • pccA complementation group
  • PCCase subunit alpha
  • EC 6.4.1.3
  • propionyl-CoA carboxylase alpha chain, mitochondrial
  • propionyl Coenzyme A carboxylase, alpha polypeptide
  • propanoyl-CoA:carbon dioxide ligase alpha subunit
  • propionyl CoA carboxylase, alpha polypeptide

PTMs for PCCA

Learn more about PTMs related to PCCA.

Carboxylation
Biotinylation
Reduction
Hydroxylation
Cleavage
Oxidation

Bioinformatics Tool for PCCA

Discover related pathways, diseases and genes to PCCA. Need help? Read the Bioinformatics Tool Guide for instructions on using this tool.
 
Vizit™, under license from BioVista Inc.