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Hmg Coa Lyase Deficiency: Disease Bioinformatics

Research of Hmg Coa Lyase Deficiency has been linked to Inborn Errors Of Metabolism, Acidosis, Hypoglycemia, Metabolic Acidosis, Methylmalonic Acidemia. The study of Hmg Coa Lyase Deficiency has been mentioned in research publications which can be found using our bioinformatics tool below. Researched pathways related to Hmg Coa Lyase Deficiency include Excretion, Fatty Acid Oxidation, Urea Cycle, Methylation, Transport. These pathways complement our catalog of research reagents for the study of Hmg Coa Lyase Deficiency including antibodies and ELISA kits against 3-HYDROXY-3-METHYLGLUTARYL-COENZYME A LYASE, MEDIUM-CHAIN ACYL-COA DEHYDROGENASE, ACADM, AUH, BTD.

Hmg Coa Lyase Deficiency Bioinformatics Tool

Laverne is a handy bioinformatics tool to help facilitate scientific exploration of related genes, diseases and pathways based on co-citations. Explore more on Hmg Coa Lyase Deficiency below! For more information on how to use Laverne, please read the How to Guide.
Vizit™, under license from BioVista Inc.

Top Research Reagents

We have 465 products for the study of Hmg Coa Lyase Deficiency that can be applied to Chromatin Immunoprecipitation, Western Blot, Immunocytochemistry/Immunofluorescence, Flow Cytometry, Immunohistochemistry from our catalog of antibodies and ELISA kits.

NBP1-32767
Western Blot: HMGCL Antibody [NBP1-32767] - rat liver lysate/extract 10 % SDS-PAGE gel, antibody dilution 1:10000.Immunocytochemistry/Immunofluorescence: HMGCL Antibody [NBP1-32767] - HeLa cells were fixed in ice-cold MeOH for 5 min. Green: HMGCL protein stained by HMGCL antibody diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar = 10 um.

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, ICC/IF, IHC

NBP1-47791
Western Blot: HES-1 Antibody (4H1) [NBP1-47791] -  HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY Hes1(Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-Hes1.Immunocytochemistry/Immunofluorescence: HES-1 Antibody (4H1) [NBP1-47791] - HeLa cells using anti-HES1 mouse monoclonal antibody.

Mouse Monoclonal
Species Human, Monkey
Applications WB, ChIP, ICC/IF

5 Publications
NBL1-12547
Western Blot: LIPC Overexpression Lysate (Adult Normal) [NBL1-12547] Left-Empty vector transfected control cell lysate (HEK293 cell lysate); Right -Over-expression Lysate for LIPC.


Species Human

NBP1-87408
Western Blot: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Analysis in human liver tissue.Immunocytochemistry/Immunofluorescence: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Immunofluorescent staining of human cell line U-2 OS shows localization to mitochondria. Antibody staining is shown in green.

Rabbit Polyclonal
Species Human
Applications WB, Simple Western, ICC/IF

2 Publications
NBP2-14891
Western Blot: Biotinidase/BTD Antibody [NBP2-14891] - Sample (30 ug of whole cell lysate)  A: Jurkat  7.5% SDS PAGE diluted at 1:1000Immunohistochemistry-Paraffin: Biotinidase/BTD Antibody [NBP2-14891] -  Paraffin-embedded mouse hind brain. BTD antibody [N3C3] dilution: 1:250.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, IHC, IHC-P

NBP1-89292
Western Blot: ACADM Antibody [NBP1-89292] - Staining of human kidney shows high expression.Immunocytochemistry/Immunofluorescence: ACADM Antibody [NBP1-89292] - Immunofluorescent staining of human cell line A-431 shows localization to mitochondria.

Rabbit Polyclonal
Species Human
Applications WB, ICC/IF, IHC

NBP1-52084
Western Blot: Phenylalanine Hydroxylase Antibody [NBP1-52084] - (0.1ug/ml) staining of Mouse (A) and Rat (B) Liver lysate (35ug protein in RIPA buffer). Primary incubation was 1 hour. Detected by chemiluminescence.Immunohistochemistry-Paraffin: Phenylalanine Hydroxylase Antibody [NBP1-52084] - Staining of paraffin embedded Human Kidney. Steamed antigen retrieval with citrate buffer pH 6, AP-staining.

Goat Polyclonal
Species Human, Mouse, Rat
Applications WB, IHC-P, PEP-ELISA

1 Publication
NB100-40853
Western Blot: Timeless Antibody [NB100-40853] - Samples: Whole cell lysate (0.5 or 1.0 mg per IP reaction; 20% of IP loaded) from HeLa cells prepared using NETN lysis buffer. Antibodies: Affinity purified rabbit anti-Timeless antibody NB100-40853 used for IP at 6 ug per reaction. Timeless was also immunoprecipitated by rabbit anti-Timeless antibody NB100-40852. For blotting immunoprecipitated Timeless, NB100-40853 was used at 0.4 ug/ml. Detection: Chemiluminescence with an exposure time of 30 seconds.Immunohistochemistry: Timeless Antibody [NB100-40853] - Sample: FFPE section of human ovarian carcinoma. Antibody: Affinity purified rabbit anti-Timeless (Cat. No. NB100-40853) used at a dilution of 1:200 (1ug/ml). Detection: DAB

Rabbit Polyclonal
Species Human
Applications WB, IHC, IHC-P

     1 Review

2 Publications
NBP1-81838
Western Blot: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Analysis in human cell line SK-MEL-30.Immunohistochemistry-Paraffin: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Staining of human liver shows low expression as expected.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, IHC, IHC-P

1 Publication
AF4096
Western blot shows lysates of HeLa human cervical epithelial carcinoma cell line. PVDF Membrane was probed with 1 µg/mL of Sheep Anti-Human M-Cadherin/Cadherin-15 Antigen Affinity-purified Polyclonal Antibody (Catalog # AF4096) followed by HRP-conjugated Anti-Sheep IgG Secondary Antibody (Catalog # <A class=NoLineLink href=M‑Cadherin/Cadherin-15 was detected in immersion fixed C2C12 mouse myoblast cell line using Sheep Anti-Human M‑Cadherin/Cadherin-15 Antigen Affinity‑purified Polyclonal Antibody (Catalog # AF4096) at 10 µg/mL for 3 hours at room temperature. Cells were stained using the Northern­Lights™ 557-conjugated Anti-Mouse IgG Secondary Antibody (red; Catalog # <A class=NoLineLink href=

Sheep Polyclonal
Species Human
Applications WB, Flow, CyTOF-ready

2 Publications
NBP1-31470
Western Blot: Triosephosphate isomerase Antibody [NBP1-31470] -  Various whole cell extracts (30 ug) were separated by 15% SDS-PAGE, and the membrane was blotted with Triosephosphate isomerase antibody diluted by 1:1000. The HRP-conjugated anti-rabbit IgG antibody (NBP2-19301) was used to detect the primary antibody.Immunocytochemistry/Immunofluorescence: Triosephosphate isomerase Antibody [NBP1-31470] - HeLa cells were fixed in 4% paraformaldehyde at RT for 15 min.Green: Triosephosphate isomerase protein stained by Triosephosphate isomerase antibody [C2C3], C-term diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar = 10 um

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, ELISA, Flow

     1 Review

4 Publications
NBP1-23000
Western Blot: ARHGEF5 Antibody [NBP1-23000] - Whole cell lysate from HeLa cells. ARHGEF5 was also immunoprecipitated by rabbit anti-ARHGEF5 antibody NBP1-23001.Immunocytochemistry/Immunofluorescence: ARHGEF5 Antibody [NBP1-23000] - Human colon carcinoma. Antibody used at a dilution of 1:200 (1ug/ml).

Rabbit Polyclonal
Species Human
Applications WB, ICC/IF, IHC

NBP2-24916
Western Blot: Catalase Antibody [NBP2-24916] - Analysis in liver lysate of 1) human 2) mouse and 3) rat at 0.1 ug/ml.Immunohistochemistry-Paraffin: Catalase Antibody [NBP2-24916] - Staining of human liver tissue using an isotype control (top) and this antibody (bottom) at 5 ug/ml.

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, IHC, IHC-P

     1 Review

4 Publications
NBP1-86516
Immunohistochemistry-Paraffin: AUH Antibody [NBP1-86516] - Staining of human pancreas shows low expression as expected.Immunohistochemistry: AUH Antibody [NBP1-86516] - Staining of human stomach shows strong cytoplasmic positivity in glandular cells.

Rabbit Polyclonal
Species Human
Applications IHC, IHC-P

AF1239
Serpin F2/ alpha <sub>2</sub>‑Antiplasmin was detected in perfusion fixed frozen sections of mouse intestine using 5 µg/mL Goat Anti-Mouse Serpin F2/ alpha <sub>2</sub>‑Antiplasmin Antigen Affinity-purified Polyclonal Antibody (Catalog # AF1239) overnight at 4 °C. Tissue was stained with the Anti-Goat HRP-DAB Cell & Tissue Staining Kit  (brown; Catalog # <A class=

Goat Polyclonal
Species Mouse
Applications WB, IHC, IP

1 Publication
NBP1-87781
Western Blot: Myelin PLP Antibody [NBP1-87781] - Analysis in control (vector only transfected HEK293T lysate) and pLP1 over-expression lysate (Co-expressed with a C-terminal myc-DDK tag (3.1 kDa) in mammalian HEK293T cells).Immunohistochemistry-Paraffin: Myelin PLP Antibody [NBP1-87781] - Staining in human cerebral cortex and pancreas tissues using anti-PLP1 antibody. Corresponding PLP1 RNA-seq data are presented for the same tissues.

Rabbit Polyclonal
Species Human
Applications WB, IHC, IHC-P

     1 Review

1 Publication
NBP1-87730
Western Blot: Methionyl tRNA synthetase Antibody [NBP1-87730] - Analysis in U2OS cells transfected with control siRNA, target specific siRNA probe #1 and #2. Remaining relative intensity is presented.Immunocytochemistry/Immunofluorescence: Methionyl tRNA synthetase Antibody [NBP1-87730] - Immunofluorescent staining of human cell line U-2 OS shows localization to cytosol.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, ICC/IF, IHC

1 Publication

Related PTMs

Hmg Coa Lyase Deficiency has been studied in relation to posttranslational modifications (PTMs) including:

Alternate Names

Hmg Coa Lyase Deficiency is also known as hmg-coa lyase deficiency, 3-hydroxy-3-methylglutaryl-coa lyase deficiency, hydroxymethylglutaric aciduria, hmg coa lyase deficiency, 3-hydroxy-3-methylglutaryl-coenzyme a lyase deficiency, deficiency of hydroxymethylglutaryl-coa lyase, 3-hydroxy-3-methylglutaric aciduria, 3-oh 3-methyl glutaric aciduria, defect in leucine metabolism, 3-oh 3-ch3 glutaric aciduria, hl deficiency, 3hmg, hmg.