Submit your image related to Diseases to be featured!

Get Social

Submit your Twitter account related to Hmg Coa Lyase Deficiency to be featured!

Blogs

Submit your blog on Hmg Coa Lyase Deficiency to be featured!

Events

Submit your event on Hmg Coa Lyase Deficiency to be featured!

Videos

Submit your video on Hmg Coa Lyase Deficiency to be featured!

Charities

Submit your charity on Hmg Coa Lyase Deficiency to be featured!

Hmg Coa Lyase Deficiency: Disease Bioinformatics

Research of Hmg Coa Lyase Deficiency has been linked to Inborn Errors Of Metabolism, Acidosis, Hypoglycemia, Metabolic Acidosis, Methylmalonic Acidemia. The study of Hmg Coa Lyase Deficiency has been mentioned in research publications which can be found using our bioinformatics tool below. Researched pathways related to Hmg Coa Lyase Deficiency include Excretion, Fatty Acid Oxidation, Urea Cycle, Methylation, Transport. These pathways complement our catalog of research reagents for the study of Hmg Coa Lyase Deficiency including antibodies and ELISA kits against HMGCL, 3-HYDROXY-3-METHYLGLUTARYL-COENZYME A LYASE, HES1, LIPC, MEDIUM-CHAIN ACYL-COA DEHYDROGENASE.

Hmg Coa Lyase Deficiency Bioinformatics Tool

Laverne is a handy bioinformatics tool to help facilitate scientific exploration of related genes, diseases and pathways based on co-citations. Explore more on Hmg Coa Lyase Deficiency below! For more information on how to use Laverne, please read the How to Guide.
Vizit™, under license from BioVista Inc.

Top Research Reagents

We have 755 products for the study of Hmg Coa Lyase Deficiency that can be applied to Chromatin Immunoprecipitation, Western Blot, Immunocytochemistry/Immunofluorescence, Flow Cytometry, Immunohistochemistry from our catalog of antibodies and ELISA kits.

NBP1-32767
Western Blot: HMGCL Antibody [NBP1-32767] - rat liver lysate/extract 10 % SDS-PAGE gel, antibody dilution 1:10000.Immunocytochemistry/Immunofluorescence: HMGCL Antibody [NBP1-32767] - HeLa cells were fixed in ice-cold MeOH for 5 min. Green: HMGCL protein stained by HMGCL antibody diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar = 10 um.

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, ICC/IF, IHC

NBP1-47791
Western Blot: HES-1 Antibody (OTI4H1) [NBP1-47791] - HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY HES1 (Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 ug per lane) were separated by SDS-PAGE and immunoblotted with anti-HES1 (1:500).Immunocytochemistry/Immunofluorescence: HES-1 Antibody (OTI4H1) [NBP1-47791] - HeLa cells using anti-HES1 mouse monoclonal antibody.

Mouse Monoclonal
Species Human
Applications WB, ChIP, ICC/IF

6 Publications
NBP3-00408
ELISA: Human LIPC ELISA Kit (Colorimetric) [NBP3-00408] - Standard Curve Reference


Species Human

NBP1-87408
Western Blot: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Analysis in human liver tissue.Immunocytochemistry/Immunofluorescence: Ornithine Carbamoyltransferase Antibody [NBP1-87408] - Staining of human cell line U-2 OS shows localization to mitochondria. Antibody staining is shown in green.

Rabbit Polyclonal
Species Human
Applications WB, Simple Western, ICC/IF

2 Publications
NBP2-14891
Western Blot: Biotinidase/BTD Antibody [NBP2-14891] - Sample (30 ug of whole cell lysate)  A: Jurkat  7.5% SDS PAGE diluted at 1:1000Immunohistochemistry-Paraffin: Biotinidase/BTD Antibody [NBP2-14891] -  Paraffin-embedded mouse hind brain. BTD antibody [N3C3] dilution: 1:250.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, IHC, IHC-P

NBP2-80447
Western Blot: ACADM Antibody (JE48-09) [NBP2-80447] - Analysis of ACADM on mouse liver tissue lysate. Proteins were transferred to a PVDF membrane and blocked with 5% BSA in PBS for 1 hour at room temperature. The primary antibody (1:500) was used in 5% BSA at room temperature for 2 hours. Goat Anti-Rabbit IgG - HRP Secondary Antibody (HA1001) at 1:5,000 dilution was used for 1 hour at room temperature.Immunocytochemistry/Immunofluorescence: ACADM Antibody (JE48-09) [NBP2-80447] - ICC staining of ACADM in SiHa cells (green). Formalin fixed cells were permeabilized with 0.1% Triton X-100 in TBS for 10 minutes at room temperature and blocked with 1% Blocker BSA for 15 minutes at room temperature. Cells were probed with the primary antibody (1:100) for 1 hour at room temperature, washed with PBS. Alexa Fluor 488 Goat anti-Rabbit IgG was used as the secondary antibody at 1:100 dilution. The nuclear counter stain is DAPI (blue).

Rabbit Monoclonal
Species Human, Mouse, Rat
Applications WB, ICC/IF, IHC

NBP1-52084
Western Blot: Phenylalanine Hydroxylase Antibody [NBP1-52084] - (0.1ug/ml) staining of Mouse (A) and Rat (B) Liver lysate (35ug protein in RIPA buffer). Primary incubation was 1 hour. Detected by chemiluminescence.Immunohistochemistry-Paraffin: Phenylalanine Hydroxylase Antibody [NBP1-52084] - Staining of paraffin embedded Human Kidney. Steamed antigen retrieval with citrate buffer pH 6, AP-staining.

Goat Polyclonal
Species Human, Mouse, Rat
Applications WB, IHC, IHC-P

1 Publication
NB100-40853
Western Blot: Timeless Antibody [NB100-40853] - Detection of human and mouse Timeless by western blot. Samples: Whole cell lysate (50 µg) from HeLa, HEK293T, and mouse NIH 3T3 cells prepared using NETN lysis buffer. Antibody: Affinity purified rabbit anti-Timeless antibody NB100-40853 used for WB at 0.1 µg/ml. Detection: Chemiluminescence with an exposure time of 10 seconds.Immunohistochemistry: Timeless Antibody [NB100-40853] - Detection of human Timeless by immunohistochemistry. Sample: FFPE section of human ovarian carcinoma. Antibody: Affinity purified rabbit anti-Timeless (NB100-40853). Detection: DAB

Rabbit Polyclonal
Species Human
Applications WB, IHC, IHC-P

     1 Review

2 Publications
NBP1-81838
Western Blot: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Analysis in control (vector only transfected HEK293T lysate) and QPCT over-expression lysate (Co-expressed with a C-terminal myc-DDK tag (3.1 kDa) in mammalian HEK293T cells).Immunohistochemistry-Paraffin: Glutaminyl-peptide Cyclotransferase/QPCT Antibody [NBP1-81838] - Staining in human adrenal gland and liver tissues using anti-QPCT antibody. Corresponding QPCT RNA-seq data are presented for the same tissues.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, IHC, IHC-P

1 Publication
NBP1-88101
Immunocytochemistry/Immunofluorescence: M-Cadherin/Cadherin-15 Antibody [NBP1-88101] - Staining of human cell line RH-30 shows localization to cytosol & the Golgi apparatus. Antibody staining is shown in green.Immunohistochemistry-Paraffin: M-Cadherin/Cadherin-15 Antibody [NBP1-88101] - Staining of human cerebellum shows weak cytoplasmic positivity in cells in granular layer.

Rabbit Polyclonal
Species Human
Applications ICC/IF, IHC, IHC-P

DSKM100
 TIM-1/KIM-1/HAVCR [HRP] TIM-1/KIM-1/HAVCR [HRP]


Species Human

1 Publication
NBP1-31470
Western Blot: Triosephosphate isomerase Antibody [NBP1-31470] - Immunodetection of glycolytic enzymes within bat and human cells. Immunodetection of Eno1, Tpi1, Pgam1 and beta2-Tub (load control) in Poly I:C transfected and Control PaKiT03 cells at 4, 8 and 20 hpt. Image collected and cropped by CiteAb from the following publication (http://www.proteomesci.com/content/13/1/25), licensed under a CC-BY licence.Immunocytochemistry/Immunofluorescence: Triosephosphate isomerase Antibody [NBP1-31470] - HeLa cells were fixed in 4% paraformaldehyde at RT for 15 min. Green: Triosephosphate isomerase stained by Triosephosphate isomerase antibody [C2C3], C-term diluted at 1:500. Blue: Hoechst 33342 staining. Scale bar= 10um.

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, ELISA, Flow

     1 Review

7 Publications
NBP1-23000
Western Blot: ARHGEF5 Antibody [NBP1-23000] - Whole cell lysate from HeLa cells. ARHGEF5 was also immunoprecipitated by rabbit anti-ARHGEF5 antibody NBP1-23001.Immunohistochemistry-Paraffin: ARHGEF5 Antibody [NBP1-23000] - FFPE section of human colon carcinoma. Antibody: Affinity purified rabbit anti-APC7 used at a dilution of 1:200 (1ug/ml). Detection: DAB

Rabbit Polyclonal
Species Human
Applications WB, IHC, IHC-P

NBP2-24916
Western Blot: Catalase Antibody [NBP2-24916] - Analysis in liver lysate of 1) human 2) mouse and 3) rat at 0.1 ug/ml.Immunohistochemistry-Paraffin: Catalase Antibody [NBP2-24916] - Staining of human liver tissue using an isotype control (top) and this antibody (bottom) at 5 ug/ml.

Rabbit Polyclonal
Species Human, Mouse, Rat
Applications WB, IHC, IHC-P

     1 Review

6 Publications
NBP1-57375
Western Blot: AUH Antibody [NBP1-57375] - HepG2 cell lysate, Antibody Titration: 0.2-1 ug/mlImmunohistochemistry-Paraffin: AUH Antibody [NBP1-57375] - Human kidney Tissue, antibody concentration 4-8ug/ml. Cells with positive label: renal corpuscle cells (indicated with arrows) 400X magnification.

Rabbit Polyclonal
Species Human
Applications WB, IHC, IHC-P

AF1239
Serpin F2/ alpha <sub>2</sub>‑Antiplasmin was detected in perfusion fixed frozen sections of mouse intestine using 5 µg/mL Goat Anti-Mouse Serpin F2/ alpha <sub>2</sub>‑Antiplasmin Antigen Affinity-purified Polyclonal Antibody (Catalog # AF1239) overnight at 4 °C. Tissue was stained with the Anti-Goat HRP-DAB Cell & Tissue Staining Kit  (brown; Catalog # <A class=

Goat Polyclonal
Species Mouse
Applications WB, IHC, IP

1 Publication
NBP1-87781
Immunohistochemistry-Paraffin: Myelin PLP Antibody [NBP1-87781] - Border of a demyelinated lesion. Image from a verified customer review.Immunohistochemistry-Paraffin: Myelin PLP Antibody [NBP1-87781] - Staining of human cerebral cortex shows high expression.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, IHC, IHC-P

     1 Review

1 Publication
NBP1-87730
Western Blot: Methionyl tRNA synthetase Antibody [NBP1-87730] - Analysis in Rh30 cells transfected with control siRNA, target specific siRNA probe #1 and #2, using Anti-MARS antibody. Remaining relative intensity is presented. Loading control: Anti-GAPDH.Immunocytochemistry/Immunofluorescence: Methionyl tRNA synthetase Antibody [NBP1-87730] - Staining of human cell line U-2 OS shows localization to cytosol. Antibody staining is shown in green.

Rabbit Polyclonal
Species Human, Mouse
Applications WB, ICC/IF, IHC

1 Publication

Related PTMs

Hmg Coa Lyase Deficiency has been studied in relation to posttranslational modifications (PTMs) including:

Alternate Names

Hmg Coa Lyase Deficiency is also known as hmg-coa lyase deficiency, 3-hydroxy-3-methylglutaryl-coa lyase deficiency, hydroxymethylglutaric aciduria, hmg coa lyase deficiency, 3-hydroxy-3-methylglutaryl-coenzyme a lyase deficiency, deficiency of hydroxymethylglutaryl-coa lyase, 3-hydroxy-3-methylglutaric aciduria, 3-oh 3-methyl glutaric aciduria, defect in leucine metabolism, 3-oh 3-ch3 glutaric aciduria, hl deficiency, 3hmg, hmg.